25. Short-term clinical, functional and radiographic outcomes after mandibular distraction osteogenesis surgery to treat severe Pierre Robin Sequence
Main Article Content
Abstract
This study aimed to describe the short-term clinical, functional and radiographic outcomes of after mandibular distraction osteogenesis (MDO) surgery. A retrospective review of 34 infants with Pierre Robin Sequence who underwent mandibular distraction osteogenesis surgery was conducted at the Vietnam National Children's Hospital. Female children accounted for 52.94%, and boys were 47.06%. There were 6/34 (17.65%) patients with Pierre Robin syndrome, and 28/34 (82.35%) with Pierre Robin alone. All children had hypoplasia of the jaw bone, small jaw, crow's beak face; 33/34 (97.06%) had tongue drop, difficulty breathing, difficulty sucking; 31/34 (91.18%) had gastric reflux; and 15/34 (44/12%) had cleft palate U and V. All children needed respiratory support, with 13/34 (38.24%) were intubated and 2/34 (5.88%) received CPAP. Early results after MDO surgery showed that the gap between the upper and lower jaws was significantly reduced compared to before surgery; the length of the body and ramus, and the space behind the throat on X-ray increased significantly compared to before surgery (p < 0.05). MDO surgery is a safe and effective treatment for Pierre Robin Syndrome, and more research is needed to assess long-term outcomes after MDO surgery.
Article Details
Keywords
clinical features, X-ray, mandibular distraction osteogenesis, Pierre Robin with a severe form
References
2. Cladis F, Kumar A, Grunwaldt L, Otteson T, Ford M, Losee JE. Pierre Robin Sequence: a perioperative review. Anesth Analg. Aug 2014;119(2):400-412. doi: 10.1213/ane.0000000000000301.
3. Hultman CS. 50 Studies Every Plastic Surgeon Should Know. CRC Press; 2014.
4. Konaş E, Çalış M, Bitik O, et al. Functional outcomes of mandibular distraction for the relief of severe airway obstruction and feeding difficulties in neonates with Pierre Robin sequence. Turk J Pediatr. 2016;58(2):159-167. doi: 10.24953/turkjped.2016.02.006.
5. Marques IL, de Sousa TV, Carneiro AF, Peres SP, Barbieri MA, Bettiol H. Robin sequence: A single treatment protocol. J Pediatr (Rio J). Jan-Feb 2005;81(1):14-22.
6. Đặng Hoàng Thơm, Trần Đình Phượng, Nguyễn Văn Sơn, Phạm Tuấn Hùng, Nguyễn Thị Hà. Đánh giá kết quả sớm về chức năng sau phẫu thuật kéo giãn xương hàm dưới ở trẻ Pierre Robin sơ sinh. Tạp chí Nghiên cứu Y học. 2018;4:51-57.
7. Van Den Elzen AP, Semmekrot BA, Bongers EM, Huygen PL, Marres HA. Diagnosis and treatment of the Pierre Robin sequence: Results of a retrospective clinical study and review of the literature. Eur J Pediatr. Jan 2001;160(1):47-53. doi: 10.1007/s004310000646.
8. Meyers AB, Zei MG, Denny AD. Imaging neonates and children with Pierre Robin sequence before and after mandibular distraction osteogenesis: what the craniofacial surgeon wants to know. Pediatr Radiol. Aug 2015;45(9):1392-402. doi: 10.1007/s00247-015-3323-y.