25. Short-term clinical, functional and radiographic outcomes after mandibular distraction osteogenesis surgery to treat severe Pierre Robin Sequence

Dang Hoang Thom, Vu Ngoc Lam, Tran Thiet Son

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Abstract

This study aimed to describe the short-term clinical, functional and radiographic outcomes of after mandibular distraction osteogenesis (MDO) surgery. A retrospective review of 34 infants with Pierre Robin Sequence who underwent mandibular distraction osteogenesis surgery was conducted at the Vietnam National Children's Hospital. Female children accounted for 52.94%, and boys were 47.06%. There were 6/34 (17.65%) patients with Pierre Robin syndrome, and 28/34 (82.35%) with Pierre Robin alone. All children had hypoplasia of the jaw bone, small jaw, crow's beak face; 33/34 (97.06%) had tongue drop, difficulty breathing, difficulty sucking; 31/34 (91.18%) had gastric reflux; and 15/34 (44/12%) had cleft palate U and V. All children needed respiratory support, with 13/34 (38.24%) were intubated and 2/34 (5.88%) received CPAP. Early results after MDO surgery showed that the gap between the upper and lower jaws was significantly reduced compared to before surgery; the length of the body and ramus, and the space behind the throat on X-ray increased significantly compared to before surgery (p < 0.05). MDO surgery is a safe and effective treatment for Pierre Robin Syndrome, and more research is needed to assess long-term outcomes after MDO surgery.

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References

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