20. Evaluation of short- and medium-term outcomes of pull-through surgery for Hirschsprung’s disease at Children’s Hospital 1,2
Main Article Content
Abstract
Hirschsprung's disease is a congenital condition characterized by the absence of ganglion cells in the intestinal wall, leading to bowel obstruction and related complications. Pull-through surgery has become a standard treatment. However, postoperative complications such as perianal dermatitis, constipation, and enterocolitis (HAEC) remain significant concerns. This prospective cohort study involved 84 pediatric patients who underwent transanal lower colon surgery for Hirschsprung's disease at Children's Hospital 1 from December 2022 to June 2024 and at Children's Hospital 2 from December 2023 to June 2024, aiming to assess the short- and medium-term outcomes of this surgical technique. Exclusion criteria included patients with severe enterocolitis requiring a temporary colostomy. The primary outcomes measured were postoperative complications and the incidence of postoperative enterocolitis at 12 months. The mean age at the time of surgery was 7.2 ± 10.7 months old, with a male-to-female ratio of 5.4:1. The Swenson-like procedure was performed in 66.6% of cases, with an average operative time of 92.14 ± 33.8 minutes. The incidence of perineal cellulitis was 32.1%, with a statistically significant increase in cases among infants operated on at 1 - 3 months of age (p < 0.05). Constipation occurred in 14.4% of cases, and postoperative enterocolitis was observed in 16.7%, with a higher risk in patients with a longer aganglionic segment. Results suggested that pull -through surgery is a safe and effective method for treating Hirschsprung's disease. Perianal dermatitis after surgery is commonly seen in children aged 1-3 months.
Article Details
Keywords
Hirschsprung’s disease, Swenson-like, transanal pull-through, Hirschsprung-associated enterocolitis
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