A case report: Kawasaki disease shock syndrome
Main Article Content
Abstract
Kawasaki disease shock syndrome (KDSS) is a severe presentation of Kawasaki disease. KDSS is
rare and difficult to diagnose early. KDSS has a high rate of resistance to IVIG and can lead to coronary
artery aneurysms. We report a case of a 4-month-old male child who presented with symptoms of
Kawasaki disease (conjunctivitis, red lips, prickly tongue, palmar edema) and shock on day 4 of illness.
Shock was determined to be from other causes and the child met the diagnostic criteria for Kawasaki
disease shock syndrome. The patient was treated with IVIG and aspirin, and did not develop coronary
artery dilation. When children have symptoms and signs of Kawasaki disease with shock condition,
pediatricians need to think of KDSS for timely treatment to reduce the risks of complications and mortality.
Article Details
Keywords
Kawasaki disease, Kawasaki disease shock syndrome, coronary artery aneurysms
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