Early results of one stage surgery for blepharophimosis – ptosis – epicanthus inversus syndrome

Trần Thu Hương, Nguyễn Xuân Tịnh, Lê Thị Kim Xuân

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Abstract

This study reports the early results of one stage surgery using Y-V medial canthoplasty and medial canthal ligaments shortening and frontalis suspension to correct blepharophimosis - ptosis -epicanthus inversus (BPES) syndrome. This interventional study was conducted prospectively in 39 BPES patients treated at Vietnam National Eye Hospital from January 2017 to June 2018. The mean preoperative measurements were 18.41 ± 2.26mm for horizontal lid fissure length (HLFL), 36.13 ± 4.32mm for inner intercanthal distance (IICD) and 1.98 ± 0.30 for the IICD/HLFL ratio. The mean postoperative measurements were 22.13 ± 2.48mm for HLFL, 30.62 ± 3.98mm for IICD and 1.39 ± 0.19 for the IICD/HLFL ratio. The differences between preoperation and postoperation for HLFL, IICD, and IICD/HLFL were statistically significant (p < 0.05). After operation, 92% cases had no ptosis or mild ptosis, 92.3% cases had upper lid position symmetry, 100% cases had no inversus epicanthus, 84.6% cases had mild medial canthal scars, and 92% cases had lagophthalmos postoperatively. General success of surgery were achieved in 87.2% cases. In conclusion, postoperative complications were treated with good results. One-stage correction of BPES is safe and efficient with the surgical techniques described.

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References

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