45. ALCAPA syndrome: Clinical case report in adult patient

Nguyen Anh Huy, Tran Viet Duc, Nguyen Sinh Hien, Nguyen Thi Phuong, Vu Ngoc Tu, Bui Quang Thang, Nguyen Lan Hieu

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Abstract

Abnormal origin of the left coronary artery from the pulmonary artery (ALCAPA syndrome) is a rare congenital heart disease, often presenting with symptoms of heart failure from birth, only a very small percentage can survive until adulthood. This report presents a case of a 29-year-old female patient, who was diagnosed based on clinical manifestations, supported by exercise electrocardiography and diagnostic imaging (echocardiography, computed tomography, and percutaneous coronary angiography). The patient had coronary artery transposition surgery at Hanoi Medical University Hospital. Through this case, we discuss diagnostic strategies and treatment options in adult patients with this rare syndrome.

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References

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