Results of surgical treatment of congenital cholesteatoma in children under 6 years old at the National Ear, Nose and Throat Hospital

Le Anh Tuan, Le Hong Anh, Nguyen Hoang Huy, Dang Thi Tram Anh, Le Chung Dung

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Abstract

This study aims to describe the surgical outcomes of congenital cholesteatoma in children. The study design is a retrospective longitudinal study with 208 patients at the National Ear, Nose and Throat Hospital from 2019 to 2024. Results: The majority of patients were in the early stages Potsic I–II (83.65%) and were indicated for exploratory tympanotomy (81.3%). During surgery, cholesteatoma was usually localized in the tympanic cavity (96.2%) and the tympanic quadrant (78.36%). No complication was reported right after surgery. Three months post-surgery, 100% of the ears had well-healed tympanic membranes, with no residual lesion. Hearing tests in 58 ears showed that 68.9% had Pure Tone Audiometry (PTA) ≤ 20 dB post-surgery, decreased slightly compared to pre-surgery but was not statistically significant (p = 0.067). Follow-up of ≥ 12 months revealed 4/37 (10.8%) residual cases in the Potsic IV group. Congenital cholesteatoma-conserving surgery in children yields good anatomical and functional results, with a low residual rate, and is particularly effective in the early stages.

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References

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