Fat-containing renal tumors in children: A case report of primary renal teratoma and teratoid wilms tumor
Main Article Content
Abstract
Although macroscopic fat on imaging typically suggests benign lesions, this finding in pediatric renal tumors may represent complex pathological entities. This report presents the clinical, histopathological, and therapeutic features of two rare cases of fat-containing renal tumors. The first case involves a 3-month-old male infant with a primary mature renal teratoma, successfully managed with nephron-sparing surgery (tumor enucleation). The second case describes a 13-month-old female infant diagnosed with a teratoid Wilms tumor, who underwent a radical nephrectomy. Both patients experienced uneventful postoperative courses with no evidence of recurrence to date. The presence of adipose tissue on imaging may not be sufficient to definitively rule out malignancy. A definitive diagnosis fundamentally relies on histopathological examination, and the surgical approach should be carefully individualized based on specific lesion characteristics.
Article Details
Keywords
teratoid Wilms tumor, primary renal teratoma, fat-containing renal tumor
References
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